Bleeding disorders are conditions that impair normal blood clotting and increase the risk of excessive bleeding. This section covers inherited and acquired bleeding disorders including hemophilia, von Willebrand disease, platelet function disorders, coagulation factor deficiencies, disseminated intravascular coagulation, and rare bleeding syndromes. Learn about bleeding symptoms, laboratory investigations, coagulation testing, diagnosis, and modern treatment approaches in clinical hematology.

Illustration showing bleeding disorders and blood clotting abnormalities

Overview of inherited and acquired bleeding disorders affecting blood clotting and hemostasis.

Vascular Bleeding Disorders

Hereditary hemorrhagic telangiectasia HHT with mucocutaneous telangiectasia causing recurrent epistaxis and skin bleeding

Vascular bleeding disorders are a group of conditions in which structural abnormalities of the blood vessel wall result in bleeding manifestations such as easy bruising, petechiae, purpura, and mucocutaneous bleeding. In contrast to platelet or coagulation factor disorders, major or life-threatening hemorrhage is uncommon, with the notable exception of hereditary hemorrhagic telangiectasia (HHT). These disorders arise from inherited or acquired […]

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Hemophilia

Large hematoma bruise symptom of Hemophilia.

Hemophilia is an inherited X-linked bleeding disorder caused by deficiency or dysfunction of clotting factor VIII (hemophilia A) or factor IX (hemophilia B). The impaired coagulation results in prolonged or spontaneous bleeding, particularly into joints and muscles. Hemophilia primarily affects males, while females are typically carriers. The term hemophilia is the standard international spelling (also rendered as haemophilia in the […]

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